PRNP genotype codon 136 and 141 | N | Positive scratch test | Alopecia | Bruxism | Tremor | Ataxia | Limb weakness | Absent menace response |
---|---|---|---|---|---|---|---|---|
VV LL | 6 | 100% | 17% | 50% | 100% | 67% | 0% | 17% |
AA LL | 6 | 83% | 50% | 83% | 33% | 100% | 17% | 0% |
AA LF | 7 | 0% | 0% | 0% | 29% | 100% | 86% | 14% |
AA FF | 3 | 0% | 0% | 33% | 33% | 67% | 100% | 33% |